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Parkinsonism in Phenylketonuria: A Consequence of Dopamine Depletion?

Phenylketonuria (PKU) is caused by a deficiency or inactivity of the enzyme phenylalanine hydroxylase that converts phenylalanine (Phe) to tyrosine (Tyr). It has been proposed that a reduction of brain Tyr levels, as well as reduced activity of the key regulatory enzyme of dopamine (DA) synthesis ty...

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Pubblicato in:JIMD Rep
Autori principali: Velema, Marieke, Boot, Erik, Engelen, Marc, Hollak, Carla
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer Berlin Heidelberg 2015
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4375126/
https://ncbi.nlm.nih.gov/pubmed/25614310
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2014_386
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