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Proteus Syndrome: Report of Intra-Abdominal Lipomatosis

Proteus syndrome (PS) is an extremely rare sporadic disorder that manifests as an asymmetric, disproportionate overgrowth of any connective tissues, such as bone, fat, or epidermal nevi, in a mosaic or patchy pattern. This hamartoneoplastic syndrome was first described by Cohen and Hayden. Its preva...

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Detalles Bibliográficos
Publicado en:European J Pediatr Surg Rep
Main Authors: Erginel, Basak, Akin, Melih, Yildiz, Abdullah, Karadag, Cetin, Sever, Nihat, Tanik, Canan, Erturk, Mehmet, Dokucu, Ali Ihsan
Formato: Artigo
Idioma:Inglês
Publicado: Georg Thieme Verlag KG 2013
Assuntos:
Acceso en liña:https://ncbi.nlm.nih.gov/pmc/articles/PMC4335946/
https://ncbi.nlm.nih.gov/pubmed/25755949
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1055/s-0033-1343078
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