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Pfeiffer syndrome: Clinical and genetic findings in five Brazilian families

Pfeiffer syndrome (PS) is mainly characterized by craniosysnostosis, midface hypoplasia, great toes with partial syndactyly of the digits and broad and medially deviated thumbs. It is caused by allelic mutations in the fibroblast growth factor receptor 1 and 2 (FGFR1 and 2) genes. This study describ...

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Dettagli Bibliografici
Pubblicato in:Med Oral Patol Oral Cir Bucal
Autori principali: Júnior, Hercílio-Martelli, de Aquino, Sibele-Nascimento, Machado, Renato-Assis, Leão, Letícia-Lima, Coletta, Ricardo- Della, Burle-Aguiar, Marcos-José
Natura: Artigo
Lingua:Inglês
Pubblicazione: Medicina Oral S.L. 2015
Soggetti:
Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4320421/
https://ncbi.nlm.nih.gov/pubmed/25129254
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4317/medoral.20032
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