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Lipoid proteinosis (Urbach-Wiethe disease) in two siblings

Lipoid proteinosis is a very rare autosomal recessive disorder characterized by deposition of hyaline material in the skin and the upper aerodigestive tract. Hoarseness of voice occurs very early in life and airway obstruction may occur. Characteristic skin lesions include multiple brown atrophic sc...

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Detalhes bibliográficos
Publicado no:Indian Dermatol Online J
Main Authors: Thaddanee, Rekha, Khilnani, Ajeet Kumar, Pandya, Purna, Chaturvedi, Mayank
Formato: Artigo
Idioma:Inglês
Publicado em: Medknow Publications & Media Pvt Ltd 2014
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Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4290189/
https://ncbi.nlm.nih.gov/pubmed/25593816
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/2229-5178.146168
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