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Berardinelli-Seip congenital lipodystrophy in two siblings

Berardinelli-Seip congenital lipodystrophy (BSCL) is a very rare autosomal recessive disorder characterized by various dermatological and systemic manifestations such as lipoatrophy, hypertriglyceridemia, hepatomegaly, acanthosis nigricans, and acromegaloid features. BSCL type 2 is more common and s...

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Foilsithe in:Indian Dermatol Online J
Main Authors: Rao, T. S. Mohana, Chennamsetty, Kavya
Formáid: Artigo
Teanga:Inglês
Foilsithe: Medknow Publications & Media Pvt Ltd 2014
Ábhair:
Rochtain Ar Líne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4252944/
https://ncbi.nlm.nih.gov/pubmed/25506557
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/2229-5178.144511
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