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Pyrophosphohydrolase activity and inorganic pyrophosphate content of cultured human skin fibroblasts. Elevated levels in some patients with calcium pyrophosphate dihydrate deposition disease.

In calcium pyrophosphate dihydrate (CPPD) crystal deposition disease, metabolic abnormalities favoring extracellular inorganic pyrophosphate (PPi) accumulation have been suspected. Elevations of intracellular PPi in cultured skin fibroblasts from a single French kindred with familial CPPD deposition...

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Dades bibliogràfiques
Publicat a:J Clin Invest
Autors principals: Ryan, L M, Wortmann, R L, Karas, B, Lynch, M P, McCarty, D J
Format: Artigo
Idioma:Inglês
Publicat: American Society for Clinical Investigation 1986
Matèries:
Accés en línia:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC424575/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/3009553/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI112487
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