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Prions in Variably Protease-Sensitive Prionopathy: An Update

Human prion diseases, including sporadic, familial, and acquired forms such as Creutzfeldt-Jakob disease (CJD), are caused by prions in which an abnormal prion protein (PrP(Sc)) derived from its normal cellular isoform (PrP(C)) is the only known component. The recently-identified variably protease-s...

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Détails bibliographiques
Publié dans:Pathogens
Auteurs principaux: Zou, Wen-Quan, Gambetti, Pierluigi, Xiao, Xiangzhu, Yuan, Jue, Langeveld, Jan, Pirisinu, Laura
Format: Artigo
Langue:Inglês
Publié: MDPI 2013
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4235694/
https://ncbi.nlm.nih.gov/pubmed/25437202
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/pathogens2030457
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