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Nutritional Status Evaluation in Patients Affected by Bethlem Myopathy and Ullrich Congenital Muscular Dystrophy

Collagen VI mutations lead to disabling myopathies like Bethlem myopathy (BM) and Ullrich congenital muscular dystrophy (UCMD). We have investigated the nutritional and metabolic status of one UCMD and seven BM patients (five female, three male, mean age 31 ± 9 years) in order to find a potential me...

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Publicat a:Front Aging Neurosci
Autors principals: Toni, Silvia, Morandi, Riccardo, Busacchi, Marcello, Tardini, Lucia, Merlini, Luciano, Battistini, Nino Carlo, Pellegrini, Massimo
Format: Artigo
Idioma:Inglês
Publicat: Frontiers Media S.A. 2014
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4235079/
https://ncbi.nlm.nih.gov/pubmed/25477818
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fnagi.2014.00315
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