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Gaucher disease with jawbone involvement: a case report

INTRODUCTION: Gaucher disease is an autosomal recessive systemic condition, and the most common of the lysosomal storage disorders. It is characterized by lipid accumulation in certain cells and organs, particularly macrophages, which appear on light microscopy as ’Gaucher cells’ or vacuolated lipid...

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Pubblicato in:J Med Case Rep
Autori principali: Ahmadieh, Azadeh, Farnad, Fariborz, Sedghizadeh, Parish P
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4234523/
https://ncbi.nlm.nih.gov/pubmed/25370695
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1752-1947-8-360
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