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Case for diagnosis

The Osler-Weber-Rendu syndrome or Hereditary Hemorrhagic Telangiectasia (HHT) is a systemic fibrovascular dysplasia characterized by defects in the elastic and vascular walls of blood vessels, making them varicose and prone to disruptions. Lesions occur in different organs and can lead to hemorrhage...

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Bibliografski detalji
Izdano u:An Bras Dermatol
Glavni autori: Boza, Juliana Catucci, Dorn, Timotio Volnei, de Oliveira, Fabiana Bazanella, Bakos, Renato Marchiori
Format: Artigo
Jezik:Inglês
Izdano: Sociedade Brasileira de Dermatologia 2014
Teme:
Online pristup:https://ncbi.nlm.nih.gov/pmc/articles/PMC4230676/
https://ncbi.nlm.nih.gov/pubmed/25387512
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1590/abd1806-4841.20143232
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