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Idiopathic Pleuroparenchymal Fibroelastosis Presenting in Recurrent Pneumothorax: A Case Report

Idiopathic pleuroparenchymal fibroelastosis (PPFE) is a rare, recently classified entity that consists of pleural and subjacent parenchymal fibrosis predominantly in the upper lungs. In an official American Thoracic Society/European Respiratory Society statement in 2013, this disease is introduced a...

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Autores principales: Noh, Hyun Jin, Seo, Yun, Huo, Sol Mi, Kim, Tae Jung, Kim, Hyo Lim, Song, Jeong Sup
Formato: Artigo
Lenguaje:Inglês
Publicado: The Korean Academy of Tuberculosis and Respiratory Diseases 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4217035/
https://ncbi.nlm.nih.gov/pubmed/25368665
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4046/trd.2014.77.4.184
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