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Mutational Spectrum of the CTNS Gene in Egyptian Patients with Nephropathic Cystinosis

Background: Nephropathic cystinosis is a rare autosomal recessive disorder caused by mutations in the CTNS gene, encoding for cystinosin, a carrier protein transporting cystine out of lysosomes. Its deficiency leads to cystine accumulation and cell damage in multiple organs, especially in the kidney...

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Dettagli Bibliografici
Autori principali: Soliman, Neveen A., Elmonem, Mohamed A., van den Heuvel, Lambertus, Abdel Hamid, Rehab H., Gamal, Mohamed, Bongaers, Inge, Marie, Sandrine, Levtchenko, Elena
Natura: Artigo
Lingua:Inglês
Pubblicazione: Springer Berlin Heidelberg 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4213330/
https://ncbi.nlm.nih.gov/pubmed/24464559
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2013_288
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