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Altered cross-bridge properties in skeletal muscle dystrophies

Force and motion generated by skeletal muscle ultimately depends on the cyclical interaction of actin with myosin. This mechanical process is regulated by intracellular Ca(2+) through the thin filament-associated regulatory proteins i.e.; troponins and tropomyosin. Muscular dystrophies are a group o...

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Autori principali: Guellich, Aziz, Negroni, Elisa, Decostre, Valérie, Demoule, Alexandre, Coirault, Catherine
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4196474/
https://ncbi.nlm.nih.gov/pubmed/25352808
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fphys.2014.00393
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