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Left ventricular systolic function and the pattern of late-gadolinium-enhancement independently and additively predict adverse cardiac events in muscular dystrophy patients

BACKGROUND: Cardiac involvement is a frequent finding in patients with Duchenne (DMD) and Becker (BMD) muscular dystrophies. With this study, we aimed at elucidating the relationship between the phenotypic expression of cardiac involvement and the occurrence of adverse cardiac events in DMD/BMD pati...

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Autores principales: Florian, Anca, Ludwig, Anna, Engelen, Markus, Waltenberger, Johannes, Rösch, Sabine, Sechtem, Udo, Yilmaz, Ali
Formato: Artigo
Lenguaje:Inglês
Publicado: BioMed Central 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4176580/
https://ncbi.nlm.nih.gov/pubmed/25315351
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/s12968-014-0081-1
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