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Genetic Features of Late Onset Primary Hemophagocytic Lymphohistiocytosis in Adolescence or Adulthood

Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening condition of uncontrolled immune activation leading to extreme inflammation. Primary HLH was once believed to be a disease that occurred only in infancy or young children, and was rarely diagnosed in adults. It is now understood that pat...

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Detalhes bibliográficos
Main Authors: Wang, Yini, Wang, Zhao, Zhang, Jia, Wei, Qing, Tang, Ran, Qi, Junyuan, Li, Lihong, Ye, Liping, Wang, Jijun, Ye, Ling
Formato: Artigo
Idioma:Inglês
Publicado em: Public Library of Science 2014
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4169386/
https://ncbi.nlm.nih.gov/pubmed/25233452
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1371/journal.pone.0107386
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