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Pseudomonas aeruginosa triggers CFTR-mediated airway surface liquid secretion in swine trachea

Cystic fibrosis (CF) is an autosomal recessive genetic disorder caused by mutations in the gene encoding for the anion channel cystic fibrosis transmembrane conductance regulator (CFTR). Several organs are affected in CF, but most of the morbidity and mortality comes from lung disease. Recent data s...

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Détails bibliographiques
Auteurs principaux: Luan, Xiaojie, Campanucci, Verónica A., Nair, Manoj, Yilmaz, Orhan, Belev, George, Machen, Terry E., Chapman, Dean, Ianowski, Juan P.
Format: Artigo
Langue:Inglês
Publié: National Academy of Sciences 2014
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC4156708/
https://ncbi.nlm.nih.gov/pubmed/25136096
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1406414111
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