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Pseudomonas aeruginosa triggers CFTR-mediated airway surface liquid secretion in swine trachea

Cystic fibrosis (CF) is an autosomal recessive genetic disorder caused by mutations in the gene encoding for the anion channel cystic fibrosis transmembrane conductance regulator (CFTR). Several organs are affected in CF, but most of the morbidity and mortality comes from lung disease. Recent data s...

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Autores principales: Luan, Xiaojie, Campanucci, Verónica A., Nair, Manoj, Yilmaz, Orhan, Belev, George, Machen, Terry E., Chapman, Dean, Ianowski, Juan P.
Formato: Artigo
Lenguaje:Inglês
Publicado: National Academy of Sciences 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4156708/
https://ncbi.nlm.nih.gov/pubmed/25136096
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.1406414111
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