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Characteristics of Patients with Cystic Fibrosis: Experience in a Large Referral Children’s Hospital in Tehran, Iran

BACKGROUND Cystic fibrosis (CF) is an autosomal recessive disease caused by a CF trans-membrane regulator (CFTR) defect. Its prevalence is 1:2500 in Caucasians, 1:15300 among African Americans and is rare in Southeast Asia. The present study aims to review demographic data, clinical manifestations a...

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Detalhes bibliográficos
Main Authors: Khatami, GR, Mir-Nasseri, MM, Seyghali, F, Allah-Verdi, B, Yourdkhani, F
Formato: Artigo
Idioma:Inglês
Publicado em: Iranian Association of Gastroerterology and Hepatology 2010
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC4154902/
https://ncbi.nlm.nih.gov/pubmed/25197508
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