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Upper Respiratory System Involvement as the Only Manifestation of Granulomatosis with Polyangiitis in a Child with Marfan Phenotype

We report a 9-year old girl with an unusual presentation of granulomatosis with polyangiitis in association with Marfan phenotype. The patient presented with recurrent sinusitis, epistaxis, hearing loss and hyperplastic gingivitis, without any signs or symptoms of major organ involvement.

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Autori principali: Amin, Reza, Alyasin, Soheila, Momen, Tooba, Khoshkhouy, Maryam, Darougar, Sepideh
Natura: Artigo
Lingua:Inglês
Pubblicazione: National Research Institute of Tuberculosis and Lung Disease 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4153231/
https://ncbi.nlm.nih.gov/pubmed/25191453
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