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The LYR factors SDHAF1 and SDHAF3 mediate maturation of the iron-sulfur subunit of succinate dehydrogenase

Disorders arising from impaired assembly of succinate dehydrogenase (SDH) result in a myriad of pathologies, consistent with its unique role in linking the citric acid cycle and electron transport chain. In spite of this critical function, however, only a few factors are known to be required for SDH...

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Autores principales: Na, Un, Yu, Wendou, Cox, James, Bricker, Daniel K., Brockmann, Knut, Rutter, Jared, Thummel, Carl S., Winge, Dennis R.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4126850/
https://ncbi.nlm.nih.gov/pubmed/24954417
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.cmet.2014.05.014
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