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Massive Spontaneous Hemothorax, Giant Intrathoracic Meningocele, and Kyphoscoliosis in Neurofibromatosis Type 1

Neurofibromatosis type 1 (NF-1) is a heterogeneous autosomal dominant disease with an incidence ranging from 1 in 2500 to 1 in 3000. Rare intrathoracic vascular disorders resulting in massive spontaneous hemothorax with fatal consequences may occur in these patients, so also are various types of ske...

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Autors principals: Yusuf, Ayodeji Salman, Pillai, Ashok, Menon, Sajesh K., Panikar, Dilip
Format: Artigo
Idioma:Inglês
Publicat: Medknow Publications & Media Pvt Ltd 2014
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4090979/
https://ncbi.nlm.nih.gov/pubmed/25013551
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4103/2006-8808.135151
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