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Sporadic inclusion body myositis: the genetic contributions to the pathogenesis

Sporadic inclusion body myositis (sIBM) is the commonest idiopathic inflammatory muscle disease in people over 50 years old. It is characterized by slowly progressive muscle weakness and atrophy, with typical pathological changes of inflammation, degeneration and mitochondrial abnormality in affecte...

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Autores principales: Gang, Qiang, Bettencourt, Conceição, Machado, Pedro, Hanna, Michael G, Houlden, Henry
Formato: Artigo
Lenguaje:Inglês
Publicado: BioMed Central 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4071018/
https://ncbi.nlm.nih.gov/pubmed/24948216
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1750-1172-9-88
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