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Pulmonary alveolar proteinosis in children on La Réunion Island: a new inherited disorder?

BACKGROUND: Pulmonary alveolar proteinosis (PAP) is very rare in children. Only a few small series have been published, with little information about long-term progression. The objective of our study was to describe the clinical, radiological and pathological features, and the long-term course of PA...

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Autori principali: Enaud, Laurent, Hadchouel, Alice, Coulomb, Aurore, Berteloot, Laureline, Lacaille, Florence, Boccon-Gibod, Liliane, Boulay, Vincent, Darcel, Françoise, Griese, Matthias, Linard, Mélinée, Louha, Malek, Renouil, Michel, Rivière, Jean-Pierre, Toupance, Bruno, Verkarre, Virginie, Delacourt, Christophe, de Blic, Jacques
Natura: Artigo
Lingua:Inglês
Pubblicazione: BioMed Central 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC4062771/
https://ncbi.nlm.nih.gov/pubmed/24927752
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1750-1172-9-85
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