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Salvage therapy with high dose Intravenous Immunoglobulins in acquired Von Willebrand Syndrome and unresponsive severe intestinal bleeding

A 91-year-old woman affected with acquired Von Willebrand (VW) syndrome and intestinal angiodysplasias presented with severe gastrointestinal bleeding (hemoglobin 5 g/dl). Despite replacement therapy with VW factor/factor VIII concentrate qid, bleeding did not stop (eleven packed red blood cell unit...

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Autores principales: Cugno, Massimo, Tedeschi, Alberto, Siboni, Simona Maria, Stufano, Francesca, Depetri, Federica, Franchi, Franca, Griffini, Samantha, Peyvandi, Flora
Formato: Artigo
Lenguaje:Inglês
Publicado: BioMed Central 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4055248/
https://ncbi.nlm.nih.gov/pubmed/24926417
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/2162-3619-3-15
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