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Tuberous Sclerosis and Fulminant Lupus in a Young Woman

Tuberous sclerosis is an autosomal dominant disorder characterized by involvement of skin, nervous system, kidneys, and lungs. It results from mutations in 1 of 2 genes: TSC1 (encoding hamartin) or TSC2 (encoding tuberin), leading to dysregulation and activation of the mammalian target of rapamycin...

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Autores principales: Singh, Namrata, Birkenbach, Mark, Caza, Tiffany, Perl, Andras, Cohen, Philip L.
Formato: Artigo
Lenguaje:Inglês
Publicado: 2013
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC4034128/
https://ncbi.nlm.nih.gov/pubmed/23519178
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/RHU.0b013e318289c033
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