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Differential motor neuron involvement in progressive muscular atrophy: a comparative study with amyotrophic lateral sclerosis

OBJECTIVE: Progressive muscular atrophy (PMA) is a clinical diagnosis characterised by progressive lower motor neuron (LMN) symptoms/signs with sporadic adult onset. It is unclear whether PMA is simply a clinical phenotype of amyotrophic lateral sclerosis (ALS) in which upper motor neuron (UMN) sign...

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Autors principals: Riku, Yuichi, Atsuta, Naoki, Yoshida, Mari, Tatsumi, Shinsui, Iwasaki, Yasushi, Mimuro, Maya, Watanabe, Hirohisa, Ito, Mizuki, Senda, Jo, Nakamura, Ryoichi, Koike, Haruki, Sobue, Gen
Format: Artigo
Idioma:Inglês
Publicat: BMJ Publishing Group 2014
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Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC4025414/
https://ncbi.nlm.nih.gov/pubmed/24833696
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1136/bmjopen-2014-005213
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