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Neurobehavioral Features and Natural History of Juvenile Neuronal Ceroid Lipofuscinosis (Batten Disease)

Juvenile neuronal ceroid lipofuscinosis is a childhood-onset neurodegenerative disease with prominent symptoms comprising a pediatric dementia syndrome: intellectual decline, mood and behavioral impairments, and loss of adaptive skills. We review the history of neurobehavioral features in juvenile n...

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Autori principali: Adams, Heather R, Mink, Jonathan W
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3976549/
https://ncbi.nlm.nih.gov/pubmed/24014508
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1177/0883073813494813
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