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Cytophagic histiocytic panniculitis, hemophagocytic lymphohistiocytosis and undetermined autoimmune disorder: reconciling the puzzle

Cytophagic histiocytic panniculitis is a rare disease, associated with either nonmalignant conditions or subcutaneous panniculitis-like T-cell lymphoma, and often also associated with hemophagocytic lymphohistiocytosis (HLH). We report the case of a 11-year-old boy with a history of secondary HLH wh...

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Библиографические подробности
Главные авторы: Pasqualini, Claudia, Jorini, Mauro, Carloni, Ines, Giangiacomi, Mirella, Cetica, Valentina, Aricò,, Maurizio, de Benedictis, Fernando Maria
Формат: Artigo
Язык:Inglês
Опубликовано: BioMed Central 2014
Предметы:
Online-ссылка:https://ncbi.nlm.nih.gov/pmc/articles/PMC3974103/
https://ncbi.nlm.nih.gov/pubmed/24524345
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1824-7288-40-17
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