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Autonomic dysfunction in muscular dystrophy: a theoretical framework for muscle reflex involvement

Muscular dystrophies are a heterogeneous group of genetically inherited disorders whose most prominent clinical feature is progressive degeneration of skeletal muscle. In several forms of the disease, the function of cardiac muscle is likewise affected. The primary defect in this group of diseases i...

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Autori principali: Smith, Scott A., Downey, Ryan M., Williamson, Jon W., Mizuno, Masaki
Natura: Artigo
Lingua:Inglês
Pubblicazione: Frontiers Media S.A. 2014
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3927082/
https://ncbi.nlm.nih.gov/pubmed/24600397
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3389/fphys.2014.00047
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