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Noninvasive ventilation reduces energy expenditure in amyotrophic lateral sclerosis

BACKGROUND: Amyotrophic lateral sclerosis (ALS) leads to chronic respiratory failure. Diaphragmatic dysfunction, a major driver of dyspnea and mortality, is associated with a shift of the burden of ventilation to extradiaphragmatic inspiratory muscles, including neck muscles. Besides, energy expendi...

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Autores principales: Georges, Marjolaine, Morélot-Panzini, Capucine, Similowski, Thomas, Gonzalez-Bermejo, Jesus
Formato: Artigo
Lenguaje:Inglês
Publicado: BioMed Central 2014
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3922008/
https://ncbi.nlm.nih.gov/pubmed/24507664
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/1471-2466-14-17
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