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Acute metabolic decompensation due to influenza in a mouse model of ornithine transcarbamylase deficiency

The urea cycle functions to incorporate ammonia, generated by normal metabolism, into urea. Urea cycle disorders (UCDs) are caused by loss of function in any of the enzymes responsible for ureagenesis, and are characterized by life-threatening episodes of acute metabolic decompensation with hyperamm...

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Autors principals: McGuire, Peter J., Tarasenko, Tatiana N., Wang, Tony, Levy, Ezra, Zerfas, Patricia M., Moran, Thomas, Lee, Hye Seung, Bequette, Brian J., Diaz, George A.
Format: Artigo
Idioma:Inglês
Publicat: The Company of Biologists Limited 2014
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3917241/
https://ncbi.nlm.nih.gov/pubmed/24271778
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1242/dmm.013003
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