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Chiari 1 Malformation and Holocord Syringomyelia in Hunter Syndrome
Compressive cervical myelopathy is a well-known life-threatening complication in mucopolysaccharidosis (MPS) patients. Glycosaminoglycan accumulation in the growing cartilage results in dens dysplasia, atlanto-axial instability, and subsequent periodontoid fibrocartilaginous tissue deposition with u...
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| Principais autores: | , , , , , , |
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| Formato: | Artigo |
| Idioma: | Inglês |
| Publicado em: |
Springer International Publishing
2013
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| Assuntos: | |
| Acesso em linha: | https://ncbi.nlm.nih.gov/pmc/articles/PMC3897861/ https://ncbi.nlm.nih.gov/pubmed/23818180 https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2013_241 |
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