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Chiari 1 Malformation and Holocord Syringomyelia in Hunter Syndrome

Compressive cervical myelopathy is a well-known life-threatening complication in mucopolysaccharidosis (MPS) patients. Glycosaminoglycan accumulation in the growing cartilage results in dens dysplasia, atlanto-axial instability, and subsequent periodontoid fibrocartilaginous tissue deposition with u...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile Nagusiak: Manara, Renzo, Concolino, Daniela, Rampazzo, Angelica, Zanetti, Alessandra, Tomanin, Rossella, Faggin, Roberto, Scarpa, Maurizio
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Springer International Publishing 2013
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3897861/
https://ncbi.nlm.nih.gov/pubmed/23818180
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1007/8904_2013_241
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