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Friedreich ataxia: metal dysmetabolism in dorsal root ganglia

BACKGROUND: Friedreich ataxia (FA) causes distinctive lesions of dorsal root ganglia (DRG), including neuronal atrophy, satellite cell hyperplasia, and absorption of dying nerve cells into residual nodules. Two mechanisms may be involved: hypoplasia of DRG neurons from birth and superimposed iron (F...

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Autores principales: Koeppen, Arnulf H, Kuntzsch, Erik C, Bjork, Sarah T, Ramirez, R Liane, Mazurkiewicz, Joseph E, Feustel, Paul J
Formato: Artigo
Lenguaje:Inglês
Publicado: BioMed Central 2013
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3893523/
https://ncbi.nlm.nih.gov/pubmed/24252376
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1186/2051-5960-1-26
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