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Mevalonate Kinase Deficiency and Neuroinflammation: Balance between Apoptosis and Pyroptosis

Mevalonic aciduria, a rare autosomal recessive disease, represents the most severe form of the periodic fever, known as Mevalonate Kinase Deficiency. This disease is caused by the mutation of the MVK gene, which codes for the enzyme mevalonate kinase, along the cholesterol pathway. Mevalonic aciduri...

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Detalhes bibliográficos
Main Authors: Tricarico, Paola Maura, Marcuzzi, Annalisa, Piscianz, Elisa, Monasta, Lorenzo, Crovella, Sergio, Kleiner, Giulio
Formato: Artigo
Idioma:Inglês
Publicado em: Molecular Diversity Preservation International (MDPI) 2013
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3876043/
https://ncbi.nlm.nih.gov/pubmed/24287904
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms141223274
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