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Mevalonate Kinase Deficiency and Neuroinflammation: Balance between Apoptosis and Pyroptosis

Mevalonic aciduria, a rare autosomal recessive disease, represents the most severe form of the periodic fever, known as Mevalonate Kinase Deficiency. This disease is caused by the mutation of the MVK gene, which codes for the enzyme mevalonate kinase, along the cholesterol pathway. Mevalonic aciduri...

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Autores principales: Tricarico, Paola Maura, Marcuzzi, Annalisa, Piscianz, Elisa, Monasta, Lorenzo, Crovella, Sergio, Kleiner, Giulio
Formato: Artigo
Lenguaje:Inglês
Publicado: Molecular Diversity Preservation International (MDPI) 2013
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Acceso en línea:https://ncbi.nlm.nih.gov/pmc/articles/PMC3876043/
https://ncbi.nlm.nih.gov/pubmed/24287904
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.3390/ijms141223274
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