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Primary Carnitine Deficiency and Cardiomyopathy

Carnitine is essential for the transfer of long-chain fatty acids from the cytosol into mitochondria for subsequent β-oxidation. A lack of carnitine results in impaired energy production from long-chain fatty acids, especially during periods of fasting or stress. Primary carnitine deficiency (PCD) i...

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Autori principali: Fu, Lijun, Huang, Meirong, Chen, Shubao
Natura: Artigo
Lingua:Inglês
Pubblicazione: The Korean Society of Cardiology 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3875693/
https://ncbi.nlm.nih.gov/pubmed/24385988
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.4070/kcj.2013.43.12.785
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