Biosynthesis and maturation of peroxisomal beta-oxidation enzymes in fibroblasts in relation to the Zellweger syndrome and infantile Refsum disease.

The biosynthesis of the peroxisomal enzymes acyl-CoA oxidase, 3-oxoacyl-CoA thiolase (acetyl-CoA acyl-transferase, EC 2.3.1.16), and catalase (EC 1.11.1.6) was studied in cultured skin fibroblasts from a control subject and from patients with Zellweger syndrome and the infantile form of Refsum disea...

Description complète

Enregistré dans:
Détails bibliographiques
Auteurs principaux: Schram, A W, Strijland, A, Hashimoto, T, Wanders, R J, Schutgens, R B, van den Bosch, H, Tager, J M
Format: Artigo
Langue:Inglês
Publié: 1986
Sujets:
Research Article
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC386458/
https://ncbi.nlm.nih.gov/pubmed/2426710
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!

Documents similaires