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Right Ventricular Dysfunction in Systemic Sclerosis Associated Pulmonary Arterial Hypertension

BACKGROUND: Systemic sclerosis associated pulmonary artery hypertension (SScPAH) has a worse prognosis compared to idiopathic pulmonary arterial hypertension (IPAH), with a median survival of 3 years after diagnosis often due to right ventricular (RV) failure. We tested if SScPAH or systemic scleros...

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Autori principali: Tedford, Ryan J., Mudd, James O., Girgis, Reda E., Mathai, Stephen C., Zaiman, Ari L., Housten-Harris, Traci, Boyce, Danielle, Kelemen, Benjamin W., Bacher, Anita C., Shah, Ami A., Hummers, Laura K., Wigley, Fredrick M., Russell, Stuart D., Saggar, Rajeev, Saggar, Rajan, Maughan, W. Lowell, Hassoun, Paul M., Kass, David A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3815697/
https://ncbi.nlm.nih.gov/pubmed/23797369
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1161/CIRCHEARTFAILURE.112.000008
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