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Pregnancies in Glycogen Storage Disease Type Ia

OBJECTIVE: Reports on pregnancies in women with GSD-Ia are scarce. Due to improved life expectancy, pregnancy is becoming an important issue. We describe 15 pregnancies focusing on dietary treatment, biochemical parameters and GSD-Ia complications. STUDY DESIGN: Carbohydrate requirements (mg/kg/min)...

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Huvudupphovsmän: Martens, Daniëlle HJ, Rake, Jan Peter, Schwarz, Martin, Ullrich, Kurt, Weinstein, David A, Merkel, Martin, Sauer, Pieter JJ, Smit, G Peter A
Materialtyp: Artigo
Språk:Inglês
Publicerad: 2008
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Länkar:https://ncbi.nlm.nih.gov/pmc/articles/PMC3812528/
https://ncbi.nlm.nih.gov/pubmed/18241814
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1016/j.ajog.2007.11.050
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