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Psychiatric manifestations in cerebrotendinous xanthomatosis

Cerebrotendinous xanthomatosis (CTX) is a rare and severe, but treatable, inborn disorder of bile acid biosynthesis and sterol storage with autosomal recessive inheritance and variable clinical presentation. CTX treatment consists of chenodeoxycholic acid and must be started as early as possible to...

Deskribapen osoa

Gorde:
Xehetasun bibliografikoak
Egile nagusia: Fraidakis, M J
Formatua: Artigo
Hizkuntza:Inglês
Argitaratua: Nature Publishing Group 2013
Gaiak:
Sarrera elektronikoa:https://ncbi.nlm.nih.gov/pmc/articles/PMC3784765/
https://ncbi.nlm.nih.gov/pubmed/24002088
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1038/tp.2013.76
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