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Late-Onset Ornithine Carbamoyltransferase Deficiency Accompanying Acute Pancreatitis and Hyperammonemia

Hyperammonemia related to urea cycle disorders is a rare cause of potentially fatal encephalopathy that is encountered in intensive care units (ICUs). Left undiagnosed, this condition may manifest irreversible neuronal damage. However, timely diagnosis and treatment initiation can be facilitated sim...

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Detalhes bibliográficos
Main Authors: Machado, Marcel Cerqueira Cesar, Fonseca, Gilton Marques, Jukemura, José
Formato: Artigo
Idioma:Inglês
Publicado em: Hindawi Publishing Corporation 2013
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC3773375/
https://ncbi.nlm.nih.gov/pubmed/24073003
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1155/2013/903546
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