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Nephrotic Syndrome Caused by Immune-Mediated Acquired LCAT Deficiency

Lecithin-cholesterol acyltransferase (LCAT) is an enzyme involved in maintaining cholesterol homeostasis. In familial LCAT deficiency (FLD), abnormal lipid deposition causes renal injury and nephrotic syndrome, frequently progressing to ESRD. Here, we describe a 63-year-old Japanese woman with no fa...

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Autori principali: Takahashi, Satoshi, Hiromura, Keiju, Tsukida, Mayuko, Ohishi, Yuko, Hamatani, Hiroko, Sakurai, Noriyuki, Sakairi, Toru, Ikeuchi, Hidekazu, Kaneko, Yoriaki, Maeshima, Akito, Kuroiwa, Takashi, Yokoo, Hideaki, Aoki, Takeo, Nagata, Michio, Nojima, Yoshihisa
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society of Nephrology 2013
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC3736715/
https://ncbi.nlm.nih.gov/pubmed/23620397
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1681/ASN.2012090913
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