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Congenital Deficiency of α(2)-Plasmin Inhibitor Associated with Severe Hemorrhagic Tendency

α(2)-Plasmin inhibitor (α(2)PI) is a recently characterized, fast-reacting plasmin inhibitor in human plasma that appears to play an important role in regulation of in vivo fibrinolysis. We report here a case of complete deficiency of α(2)PI in man. The patient, a 25-yr-old Japanese man, had a life-...

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Podrobná bibliografie
Vydáno v:J Clin Invest
Hlavní autoři: Aoki, Nobuo, Saito, Hidehiko, Kamiya, Tadashi, Koie, Katsuo, Sakata, Yoichi, Kobakura, Masateru
Médium: Artigo
Jazyk:Inglês
Vydáno: American Society for Clinical Investigation 1979
Témata:
On-line přístup:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC372028/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/156196/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI109387
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