Chargement en cours...

Upregulation of the Rab27a-Dependent Trafficking and Secretory Mechanisms Improves Lysosomal Transport, Alleviates Endoplasmic Reticulum Stress, and Reduces Lysosome Overload in Cystinosis

Cystinosis is a lysosomal storage disorder caused by the accumulation of the amino acid cystine due to genetic defects in the CTNS gene, which encodes cystinosin, the lysosomal cystine transporter. Although many cellular dysfunctions have been described in cystinosis, the mechanisms leading to these...

Description complète

Enregistré dans:
Détails bibliographiques
Auteurs principaux: Johnson, Jennifer L., Napolitano, Gennaro, Monfregola, Jlenia, Rocca, Celine J., Cherqui, Stephanie, Catz, Sergio D.
Format: Artigo
Langue:Inglês
Publié: American Society for Microbiology 2013
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC3719680/
https://ncbi.nlm.nih.gov/pubmed/23716592
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1128/MCB.00417-13
Tags: Ajouter un tag
Pas de tags, Soyez le premier à ajouter un tag!