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Heterozygote Expression in Propionyl Coenzyme A Carboxylase Deficiency

We measured propionyl coenzyme A carboxylase (PCC) activity in extracts of skin fibroblasts and peripheral blood leukocytes from controls and obligate heterozygotes for PCC deficiency. 6 heterozygotes were from the pcc A complementation group; 12 were from the other major complementation group, desi...

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Dettagli Bibliografici
Pubblicato in:J Clin Invest
Autori principali: Wolf, Barry, Rosenberg, Leon E.
Natura: Artigo
Lingua:Inglês
Pubblicazione: American Society for Clinical Investigation 1978
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Accesso online:https://ncbi.nlm.nih.govhttps://pmc.ncbi.nlm.nih.gov/articles/PMC371850/
https://ncbi.nlm.nih.govhttps://pubmed.ncbi.nlm.nih.gov/711858/
https://ncbi.nlm.nih.govhttps://doi.org/10.1172/JCI109221
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