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Synthesis and Secretion of Cystic Fibrosis Ciliary Dyskinesia Substances by Purified Subpopulations of Leukocytes

Cultured peripheral blood leukocytes (PBL) from individuals homozygous or heterozygous for the defective gene causing the inherited disease cystic fibrosis (CF) secrete three different ciliary dyskinesia substances (CDS), which can be detected by their activity in vitro in a rabbit mucociliary bioas...

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Detalhes bibliográficos
Main Authors: Wilson, Gregory B., Bahm, Valorie J.
Formato: Artigo
Idioma:Inglês
Publicado em: 1980
Assuntos:
Acesso em linha:https://ncbi.nlm.nih.gov/pmc/articles/PMC371538/
https://ncbi.nlm.nih.gov/pubmed/7430342
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