Inhibition by propionyl-coenzyme A of N-acetylglutamate synthetase in rat liver mitochondria. A possible explanation for hyperammonemia in propionic and methylmalonic acidemia.

In the search for the mechanism by which hyperammonemia complicates propionic and methylmalonic acidemia the effects of a series of acyl-coenzyme A (CoA) derivatives were studied on the activity of N-acetylglutamate synthetase in rat liver mitochondria using acetyl-CoA as substrate. Propionyl-CoA wa...

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Bibliografische gegevens
Hoofdauteurs: Coude, F X, Sweetman, L, Nyhan, W L
Formaat: Artigo
Taal:Inglês
Gepubliceerd in: 1979
Onderwerpen:
Research Article
Online toegang:https://ncbi.nlm.nih.gov/pmc/articles/PMC371306/
https://ncbi.nlm.nih.gov/pubmed/500823
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