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Unusually early presentation of small-bowel adenocarcinoma in a patient with Peutz-Jeghers syndrome

Peutz-Jeghers (PJS) syndrome is an autosomal dominant cancer predisposition syndrome characterized by melanotic macules, and hamartomatous polyps. Small-bowel surveillance in the pediatric PJS population is not designed to identify small-bowel malignancy which is thought to arise in adulthood. A 13...

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Autors principals: Wangler, Michael F., Chavan, Rishikesh, Hicks, M. John, Nuchtern, Jed.G., Hegde, Madhuri, Plon, Sharon E., Thompson, Patrick A.
Format: Artigo
Idioma:Inglês
Publicat: 2013
Matèries:
Accés en línia:https://ncbi.nlm.nih.gov/pmc/articles/PMC3708690/
https://ncbi.nlm.nih.gov/pubmed/23426006
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MPH.0b013e318282db11
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