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Human Skin Collagenase in Recessive Dystrophic Epidermolysis Bullosa: PURIFICATION OF A MUTANT ENZYME FROM FIBROBLAST CULTURES

Recessive dystrophic epidermolysis bullosa, a genodermatosis characterized by dermolytic blister formation in response to minor trauma, is characterized by an incresaed collagenase synthesis by skin fibroblasts in culture. Since preliminary studies of partially purified recessive dystrophic epidermo...

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Autori principali: Stricklin, George P., Welgus, Howard G., Bauer, Eugene A.
Natura: Artigo
Lingua:Inglês
Pubblicazione: 1982
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Accesso online:https://ncbi.nlm.nih.gov/pmc/articles/PMC370210/
https://ncbi.nlm.nih.gov/pubmed/6282934
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