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Extra-Hepatic Cholangiocyte Cilia are Abnormal in Biliary Atresia

OBJECTIVES: Biliary atresia is a rapidly progressive form of biliary fibrosis affecting neonates. We previously reported that primary cilia on the intrahepatic cholangiocytes of patients with both syndromic and non-syndromic biliary atresia were structurally abnormal. Our objective was to determine...

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Hlavní autoři: Karjoo, Sara, Hand, Nicholas J., Loarca, Lorena, Russo, Pierre A., Friedman, Joshua R., Wells, Rebecca G.
Médium: Artigo
Jazyk:Inglês
Vydáno: 2013
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On-line přístup:https://ncbi.nlm.nih.gov/pmc/articles/PMC3696479/
https://ncbi.nlm.nih.gov/pubmed/23609896
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1097/MPG.0b013e318296e525
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