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Identification of a second bovine amyloidotic spongiform encephalopathy: Molecular similarities with sporadic Creutzfeldt-Jakob disease

Transmissible spongiform encephalopathies (TSEs), or prion diseases, are mammalian neurodegenerative disorders characterized by a posttranslational conversion and brain accumulation of an insoluble, protease-resistant isoform (PrP(Sc)) of the host-encoded cellular prion protein (PrP(C)). Human and a...

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Détails bibliographiques
Auteurs principaux: Casalone, Cristina, Zanusso, Gianluigi, Acutis, Pierluigi, Ferrari, Sergio, Capucci, Lorenzo, Tagliavini, Fabrizio, Monaco, Salvatore, Caramelli, Maria
Format: Artigo
Langue:Inglês
Publié: National Academy of Sciences 2004
Sujets:
Accès en ligne:https://ncbi.nlm.nih.gov/pmc/articles/PMC365745/
https://ncbi.nlm.nih.gov/pubmed/14970340
https://ncbi.nlm.nih.govhttp://dx.doi.org/10.1073/pnas.0305777101
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